Reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them. Learn more about reticular erythematous mucinosis from related diseases, pathways, genes and ptms with the novus bioinformatics tool. Llinear morphea with secondary mucinosisinear morphea with.
Multiple lesions may indicate the carney complex in which the benign tumours may develop in the. Reticular erythematous mucinosis rem is a rare entity characterized by infiltrated erythematous plaques on exposed areas of the thorax and back. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective treatment modalities have been encouraging. Cutaneous mucinosis in mixed connective tissue disease. Aug 01, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Reticular erythematous mucinosis rem is a rare, benign skin condition that causes welldefined red rashes on the skin.
Reticular erythematous mucinosis young to middle aged people women erythematous reticular or plaquelike eruption in the middle of the chest or back photoinduction. Dermis sindrome rem o mucinosis reticular eritematosa. Pdf sindrome rem associada a lupus eritematoso sistemico e. Aug 01, 2011 includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. At present, almost 100 patients with rem syndrome have been described. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaquelike mucinosis and midline mucinosis. Papulonodular mucinosis in systemic lupus erythematosus. Mucinous disorders of the skinbeyond the dermal mucinosis. Reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Reticular erythematous mucinosis the doctors doctor. She has been on topical and oral steroids without resolution. Reticular erythematous mucinosis rem syndrome is a rare, chronic disease characterized by asymptomatic, persistent reticular, slightly infiltrated erythematous plaques on chest andor back with slight infiltration. Benign or noncancerous forms of follicular mucinosis benign, primary or.
The leading primary care society for dermatology and skin surgery. Benign or noncancerous forms of follicular mucinosis benign, primary or idiopathic follicular mucinosis are often of unknown cause. Reticular erythematous mucinosis is a chronic and rare syndrome of. Reticular erythematous mucinosis rem is a disorder of dermal mucin accumulation that has been reported throughout the world. Reticular erythematous mucinosis rem syndrome is a rare cutaneous disease first described by steigleder et al 1 more than 30 years ago. Sometimes follicular mucinosis may show up in skin biopsy results for other inflammatory skin diseases. Since it was not possible to relate these findings to any known syndrome, a combination of the main signs, reticular erythema and mucinosis, was used to name this entity rem syndrome. It is also called midline mucinosis or plaquelike cutaneous mucinosis. Focal cutaneous mucinosis see the pathology of focal cutaneous mucinosis. Reticular erythematous mucinosis definition of reticular. The cutaneous mucinoses are a heterogeneous group of diseases in which mucin accumulates in the skin or within the hair follicle. Cutaneous mucinosis covers a heterogeneous group of diseases involving a diffuse and or focal mucin accumulation in the skin and its annexes.
It is caused by mucinous infiltration of tissues, and usually involves the scalp, face, and neck. Cutaneous mucinosis in mixed connective tissue disease ncbi. What is reticular erythematous mucinosis reticular erythematous mucinosis rem is rare form of cutaneous mucinosis. Suarezamor and others published mucinosis eritematosa reticular. It is a disease that tends to affect women in the third and fourth decades of life. Although the exact etiology remains undefined, efforts to elucidate pathogenesis, disease associations, and prospective. Jul 12, 2012 reticular erythematous mucinosis rem is a rare cutaneous condition often referred to as plaque. Examination of biopsy specimen showed focal mucin deposition in papillary and upper reticular dermis. On alcian blue periodic acid schiff stain, abundant mucin deposition was demonstrated in the upper reticular dermis figure 3b. Dermis mucinose eritematosa reticulada information on the. Reticular erythematous mucinosis syndrome rem syndrome.
The area is photosensitive and has been present for 1 year without resolution and without new lesions. Reticular erythematous mucinosis primary care dermatology. This is a 28 year old woman who presents with a reticulated rash on her chest. Although the exact etiology remains undefined, efforts to. There are 0 terms under the parent term reticular erythematous mucinosis in the icd10cm alphabetical index. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most. Mucinosis eritematosa reticular actas dermosifiliograficas. Reticular erythematous mucinosis the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. Icd10cm alphabetical index reticular erythematous mucinosis. Clinical features and efficacy of antimalarial treatment for. Reticular erythematous mucinosis rem is a skin condition caused by fibroblasts producing abnormally large amounts of mucopolysaccharides.
Induction of the disease has been associated with viral processes, solar irradiation. Follicular mucinosis definition of follicular mucinosis by. Reticular erythematous mucinosis rem, rem syndrome. Llinear morphea with secondary mucinosisinear morphea. Papules small bumps develop on the midback or chest and form a netlike pattern hence the name, reticular. These are the first cases of mucinosis described in mixed connective tissue disease. Reticular erythematous mucinosis rem is a rare chronic dermatosis that is typically characterized by reticular macular erythema or erythematous papules and plaques on the central area of the chest and back of middleaged women. These are most commonly seen on the chest and upper back. Reticular erythematous mucinosis, journal of the european.
It presents with reticular, macular lesions or erythematous papules and plaques. Reticular erythematous mucinosis on the midline of the back article pdf available in cutis. Predominantly affecting middleaged women, rem syndrome skin lesions are typically located on the central area of the chest or on the upper back but may also spread to the upper abdomen. Background reticular erythematous mucinosis rem is an uncommon disease, the nosology and specific characteristics of which are controversial because most reports deal with single cases or small series. Reticular erythematous mucinosis is a rare syndrome which can be misdiagnosed as seborrhoeic dermatitis. Reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Jan 06, 2010 reticular erythematous mucinosis rem is a rare chronic dermatosis with a predilection for anterior and posterior trunk typically. Courtesy of bryan anderson, md rarely, rem may occur on the extremities, head, neck, or groin, and there has been a single report of gingival involvement in a patient with typical lesions on the chest.
Author links open overlay panel amalia serrano lourdes rodriguez julian s. Pdf reticular erythematous mucinosis on the midline of the back. Reticular erythematous mucinosis and lupus erythematosus. Is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Induction of the disease has been associated with viral processes, solar irradiation, specific.
Includes pretibial myxedema of hyperthyroidism, generalized myxedema of hypothyroidism, papillary mucinosis lichen myxedematosus, myxoid cyst, cutaneous focal mucinosis, follicular mucinosis and carneys syndrome related myxoid nodules. Mar 26, 2010 is there a home remedy for reticular erythematous mucinosis syndrome answered by a verified dermatologist we use cookies to give you the best possible experience on our website. Mucinosis eritematosa reticular actas dermosifiliogr 2004. Department of dermatology, national defense medical college, 32 namiki, tokorozawa, saitama 35985, japan. These findings point to the diagnosis of reticular mucinosis. Is there a home remedy for reticular erythematous mucinosis. Treatment of reticular erythematous mucinosis with uva1. Cutaneous focal mucinosis is a skin condition characterized by a solitary nodule or papule 189.
655 785 367 635 794 1530 502 639 1579 801 270 1578 119 432 1463 275 1387 594 1613 1428 26 1593 191 870 1507 1069 1298 1356 51 591 479 456 1352 1631 903 432 968 806 2 181 979 83 231 32 1479 1243 951 1286 1278 293 72